report of four cases of familial idiopathic pulmonary fibrosis
نویسندگان
چکیده
a 25 year old male and his 46 year old aunt presented with shortness of breath and a dramatic response to steroids. the other two patients are sisters with more advanced disease. one of these responded partially to steroids, while the other died within 4 months of treatment. the genetic basis and pathogenesis are discussed.
منابع مشابه
REPORT OF FOUR CASES OF FAMILIAL IDIOPATHIC PULMONARY FIBROSIS
A 25 year old male and his 46 year old aunt presented with shortness of breath and a dramatic response to steroids. The other two patients are sisters with more advanced disease. One of these responded partially to steroids, while the other died within 4 months of treatment. The genetic basis and pathogenesis are discussed.
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عنوان ژورنال:
medical journal of islamic republic of iranجلد ۲، شماره ۴، صفحات ۳۱۳-۳۱۶
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